From the Departments of *Nuclear Medicine, and †Diagnostic and Interventional Radiology, Hannover Medical School, Hannover, Germany.
Clin Nucl Med. 2017 Dec;42(12):e527-e528. doi: 10.1097/RLU.0000000000001864.
Carney triad is a very rare syndrome characterized by the synchronous or metachronous occurrence of gastrointestinal stromal tumors, pulmonary chondroma, and extra-adrenal paraganglioma. We present the case of a 36-year-old woman with complete Carney triad who underwent a Ga-DOTA-TATE PET/CT scan for restaging of metastasizing extra-adrenal paraganglioma and for evaluation of targeted radionuclide therapy potential. On the Ga-DOTA-TATE PET scan, increased tracer accumulation was observed in paraganglioma metastases. This case highlights the usefulness of Ga-DOTA-TATE PET/CT for restaging of metastasizing paraganglioma in Carney triad and the option of targeted radionuclide therapy in this entity.
卡尼三联征是一种非常罕见的综合征，其特征为胃肠道间质瘤、肺软骨瘤和肾上腺外副神经节瘤的同步或异时发生。我们报告了一例 36 岁的女性患者，患有完整的卡尼三联征，她接受了 Ga-DOTA-TATE PET/CT 扫描，用于转移性肾上腺外副神经节瘤的分期和评估靶向放射性核素治疗的潜力。在 Ga-DOTA-TATE PET 扫描中，观察到副神经节瘤转移部位的示踪剂积聚增加。本病例强调了 Ga-DOTA-TATE PET/CT 在卡尼三联征中用于转移性副神经节瘤分期的作用，以及在该实体中进行靶向放射性核素治疗的选择。
