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以视网膜分支动脉阻塞为表现的特发性视网膜血管炎、动脉瘤和神经视网膜炎综合征

Idiopathic Retinal Vasculitis, Aneurysms, and Neuroretinitis Syndrome Presenting With Branch Retinal Artery Occlusion.

作者信息

Zacharia Jennifer A, Chin Adam T, Rebhun Carl B, Louzada Ricardo N, Adhi Mehreen, Cole Emily D, Moreira-Neto Carlos, Waheed Nadia K, Duker Jay S

出版信息

Ophthalmic Surg Lasers Imaging Retina. 2017 Nov 1;48(11):948-951. doi: 10.3928/23258160-20171030-13.

DOI:10.3928/23258160-20171030-13
PMID:29121367
Abstract

Idiopathic retinal vasculitis, aneurysms, and neuroretinitis (IRVAN) is a rare syndrome affecting the retinal and optic disc vasculature. Diffuse retinal ischemia, macular edema, and neovascularization may lead to bilateral vision loss. The authors report a case of a 36-year-old woman presenting with branch retinal artery occlusion (BRAO) in her right eye who was subsequently diagnosed with IRVAN syndrome. She was treated with panretinal photocoagulation for peripheral retinal ischemia and pars plana vitrectomy for vitreous hemorrhage. She later developed a BRAO in her left eye. This case demonstrates that BRAO may be a presenting feature of IRVAN syndrome. [Ophthalmic Surg Lasers Imaging Retina. 2017;48:948-951.].

摘要

特发性视网膜血管炎、动脉瘤和神经视网膜炎(IRVAN)是一种影响视网膜和视盘血管系统的罕见综合征。弥漫性视网膜缺血、黄斑水肿和新生血管形成可能导致双眼视力丧失。作者报告了一例36岁女性病例,该患者右眼出现视网膜分支动脉阻塞(BRAO),随后被诊断为IRVAN综合征。她接受了全视网膜光凝治疗周边视网膜缺血,并接受了玻璃体切割术治疗玻璃体积血。后来她左眼也出现了BRAO。该病例表明,BRAO可能是IRVAN综合征的首发特征。[《眼科手术、激光与影像学杂志》。2017年;48:948 - 951。]

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引用本文的文献

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