发生于一名3岁男孩阴茎的肺泡软组织肉瘤：一例罕见病例报告。
Alveolar soft part sarcoma occurring in the penis of a 3-year-old boy: A rare case report.
作者信息
Qiu Linli, Li Yuman, Ali Shima Ibrahim, Xie Mingxing
机构信息
Department of Ultrasound, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China Radiological Science And Medical Imaging Department, Alzaiem Alazhari University, Khartoum, Sudan.
出版信息
Medicine (Baltimore). 2017 Nov;96(45):e8383. doi: 10.1097/MD.0000000000008383.
RATIONALE
Alveolar soft part sarcoma (ASPS) is a rare, malignant neoplasm, which mostly occurs in the upper and lower extremities. This article presents an unusual case of ASPS involving the penis of a 3-year-old boy. To our knowledge, this is the first case of ASPS in the penis of a child.
PATIENT CONCERNS
The patient complained of slight penile pain for 1 year and a soft tissue mass could be palpated in his penis.
DIAGNOSES
Imaging was performed on the penis. The pathological feature of the mass was evaluated through biopsy examination. It was found that the mass was an alveolar soft tissue sarcoma, which was then confirmed by immunohistochemistry.
INTERVENTIONS
The patient only underwent a partial penectomy because his parents wished to keep the penis. Conventional chemotherapy has been performed for 6 months after the surgery.
OUTCOMES
At 28-month follow-up the mass did not increase apparently, and no signs of metastasis were found.
LESSONS
ASPS may occur originally in the penis.
理论依据
肺泡软组织肉瘤（ASPS）是一种罕见的恶性肿瘤，主要发生于上下肢。本文介绍了一例累及一名3岁男孩阴茎的罕见ASPS病例。据我们所知，这是首例儿童阴茎ASPS病例。
患者情况
患者主诉阴茎轻微疼痛1年，阴茎可触及软组织肿块。
诊断
对阴茎进行了影像学检查。通过活检评估肿块的病理特征。发现肿块为肺泡软组织肉瘤，免疫组化予以确诊。
干预措施
由于患儿父母希望保留阴茎，患者仅接受了部分阴茎切除术。术后进行了6个月的常规化疗。
结果
随访28个月时，肿块无明显增大，未发现转移迹象。
经验教训
ASPS可能原发于阴茎。
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