Bansal A, Kaur M, Dalal V
National Institute of Pathology (ICMR), Safdarjang Hospital Campus, New Delhi, India.
Pathologica. 2017 Sep;109(3):168-170.
Renal replacement lipomatosis (RRL) is a rare disorder which exhibits extensive proliferation of fatty tissue within the renal sinus, hilum, and perirenal region. The pathogenesis of this entity is unknown, though association with aging, renal atrophy, longstanding chronic urinary infections has been noted. Although imaging modalities may suggest the diagnosis of this entity, it is histopathology that clinches the diagnosis most accurately. We report a case of a 52 year old male who presented with nonfunctioning kidney and was histopathologically confirmed to be a case of renal replacement lipomatosis.
肾替代脂肪瘤病（RRL）是一种罕见的疾病，其特征为肾窦、肾门及肾周区域内脂肪组织广泛增生。尽管已注意到该疾病与衰老、肾萎缩、长期慢性泌尿系统感染有关，但其发病机制尚不清楚。虽然影像学检查可能提示该疾病的诊断，但最准确确诊仍需依靠组织病理学检查。我们报告一例52岁男性患者，其患有无功能肾，经组织病理学检查确诊为肾替代脂肪瘤病。
