Khaleghnejad Ahmad, Sadr Saeed, Tabatabaei Seyyed Ahmad, Farahbakhsh Nazanin, Dabirmoghaddam Payman, Mansori Saeed Saadat
Pediatric Surgery Research Center, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Department of Pulmonology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Respir Med Case Rep. 2017 Nov 4;23:26-28. doi: 10.1016/j.rmcr.2017.10.007. eCollection 2018.
Laryngotracheoesophageal clefts (LTEC) are rare malformations which involve the upper respiratory and digestive tract. Surgical repair should be undertaken promptly to maintain a secure airway and prevent serious pulmonary aspiration. This paper reports the first case of LTEC type 3 with severe laryngotracheomalacia that was brought to Mofid children's hospital in late infancy with a poor health status. Delayed defect correction was our team strategy for the patient when she had achieved good weight gain. At the age of 22 months in collaboration with the pediatric surgical and otolaryngologist team, the repair of the laryngeal cleft was done with lateral open approach method. She was discharged with tracheostomy and gastrostomy. In the next six months follow up after the surgery tracheostomy decannulation and gastrostomy tube removal were done and the infant is now in regular follow-up.
喉气管食管裂（LTEC）是一种累及上呼吸道和消化道的罕见畸形。应及时进行手术修复，以维持气道安全并防止严重的肺误吸。本文报告了首例3型喉气管食管裂合并严重喉软化症的病例，该患儿在婴儿晚期因健康状况不佳被送至莫菲德儿童医院。当患儿体重增加良好时，我们团队对其采取了延迟缺陷矫正策略。在患儿22个月大时，与小儿外科和耳鼻喉科团队合作，采用外侧开放入路方法进行了喉裂修复。她出院时带有气管造口术和胃造口术。术后六个月随访时进行了气管造口拔管和胃造口管拔除，该婴儿目前正在接受定期随访。
