自身免疫性肝炎合并远端肾小管酸中毒及小肠部分旋转不良

Autoimmune Hepatitis with Distal Renal Tubular Acidosis and Small Bowel Partial Malrotation.

作者信息

Kanaiyalal Modi Tejas, Parikh Hardik, Sadalge Abhishek, Gupte Amit, Bhatt Pratin, Shukla Akash

机构信息

Department of Gastroenterology, Seth GS Medical College, KEM Hospital, Mumbai, Maharashtra, India.

出版信息

Euroasian J Hepatogastroenterol. 2015 Jul-Dec;5(2):107-109. doi: 10.5005/jp-journals-10018-1145. Epub 2016 Jul 9.

DOI:10.5005/jp-journals-10018-1145

PMID:29201703

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5578537/

Abstract

UNLABELLED

Renal tubular acidosis (RTA) is not uncommon in patient with chronic autoimmune hepatitis (AIH), but usually remains latent. Here, we report a case of renal tubular acidosis RTA who presented with AIH. She was also diagnosed to have partial bowel malrotation. A 9-year-old girl, a case of distal RTA, presented with jaundice, abdominal distension and altered sensorium. She was diagnosed to be AIH, which was successfully treated with steroids and azathioprine. Coexistent midgut partial malrotation with volvulus was diagnosed during the treatment. She was treated successfully with anti-tuberculous treatment for cervical lymphadenitis. Autoimmune hepatitis should not be ruled out in each case of RTA presenting with jaundice.

HOW TO CITE THIS ARTICLE

Modi TK, Parikh H, Sadalge A, Gupte A, Bhatt P, Shukla A. Autoimmune Hepatitis with Distal Renal Tubular Acidosis and Small Bowel Partial Malrotation. Euroasian J Hepato-Gastroenterol 2015;5(2):107-109.

摘要

未标注

肾小管酸中毒（RTA）在慢性自身免疫性肝炎（AIH）患者中并不罕见，但通常处于潜伏状态。在此，我们报告一例伴有AIH的肾小管酸中毒RTA病例。她还被诊断为部分肠旋转不良。一名9岁女孩，为远端RTA病例，表现为黄疸、腹胀和意识改变。她被诊断为AIH，经类固醇和硫唑嘌呤成功治疗。在治疗期间诊断出并存中肠部分旋转不良伴肠扭转。她因颈淋巴结炎接受抗结核治疗后成功治愈。每例出现黄疸的RTA病例均不应排除自身免疫性肝炎。