Luc Jessica G Y, Phan Kevin, Tchantchaleishvili Vakhtang
Faculty of Medicine and Dentistry, University of Alberta, Edmonton, Alberta, Canada.
Faculty of Medicine, University of Sydney, Sydney, New South Wales, Australia.
J Thorac Dis. 2017 Sep;9(9):3313-3318. doi: 10.21037/jtd.2017.08.101.
Primary cardiac tumors are uncommon clinical entities with an incidence of 0.0017% to 0.03% of all autopsies. Cystic tumor of the atrioventricular (AV) node, also known as mesothelioma of the AV node, is a benign congenital tumor that is located in the triangle of Koch in the AV nodal region of the atrial septum of the heart. It comprises of 2.7% of cardiac tumors and is the most common primary cardiac tumor causing sudden death. We herein review the etiology, presentation, differential diagnosis, diagnosis, management, surgical approaches and outcomes of this rare tumor.
原发性心脏肿瘤是临床罕见疾病,在所有尸检中发病率为0.0017%至0.03%。房室(AV)结囊性肿瘤,也称为AV结间皮瘤,是一种良性先天性肿瘤,位于心脏房间隔AV结区域的Koch三角区。它占心脏肿瘤的2.7%,是导致猝死的最常见原发性心脏肿瘤。我们在此回顾这种罕见肿瘤的病因、表现、鉴别诊断、诊断、管理、手术方法及预后。