Gibo H, Watanabe N, Kobayashi S, Sugita K
Department of Neurosurgery, Shinshu University School of Medicine, Matsumoto, Japan.
Surg Neurol. 1989 Feb;31(2):142-8. doi: 10.1016/0090-3019(89)90329-7.
A rare case of an arteriovenous malformation involving the optic chiasm associated with vascular anomaly in the left maxillary region is presented. The angiogram demonstrated an arteriovenous malformation arising from the anterior circle of Willis (internal carotid, posterior communicating, and proximal anterior cerebral arteries), and located in the region of the optic chiasm and hypothalamus. The case was diagnosed as the Bonnet-Dechaume-Blanc syndrome without intraorbital and retinal arteriovenous malformations. The suprasellar arteriovenous malformation was removed, except for a small portion in the hypothalamus, with satisfactory results.
本文报告一例罕见的涉及视交叉的动静脉畸形，该畸形与左上颌区域的血管异常相关。血管造影显示动静脉畸形起源于Willis环前部（颈内动脉、后交通动脉和大脑前动脉近端），位于视交叉和下丘脑区域。该病例被诊断为Bonnet-Dechaume-Blanc综合征，无眶内和视网膜动静脉畸形。除下丘脑一小部分外，切除了鞍上动静脉畸形，效果满意。
