Schrøder M, Rasmussen O V, Lauritzen A F
Ugeskr Laeger. 1989 Feb 27;151(9):566-8.
The urachus is an embryological structure originating from the allantois and situated in Retzius' space. Neoplasms originating from the urachus are very rare. They become clinically manifest late in the course of the disease. Deformation of the apex of the bladder and supravesical calcifications are described as radiological findings but these are of limited diagnostic value and should be supplemented by ultrasonic scanning, computed tomography and possibly by magnetic resonance scanning which will provide information about the extent of the disease. The final diagnosis is based on the macroscopic findings and the macroscopic picture. Three cases representing various aspects of the disease are presented. Treatment consists of en bloc resection in the form of partial cystectomy and excision of the tissue in Retzius' space and the umbilicus. The results are, however, disappointing as the five-year survival rates in the majority of materials do not exceed 10%. Irradiation is of doubtful value and chemotherapy is scarcely of value in the treatment.
脐尿管是一种起源于尿囊并位于雷济厄斯间隙的胚胎学结构。起源于脐尿管的肿瘤非常罕见。它们在疾病过程后期才会出现临床症状。膀胱顶部变形和膀胱上钙化被描述为放射学表现，但这些诊断价值有限，应通过超声扫描、计算机断层扫描，可能还需通过磁共振扫描来补充，这些检查将提供有关疾病范围的信息。最终诊断基于宏观检查结果和大体图像。本文介绍了三例代表该疾病不同方面的病例。治疗方法是整块切除，即部分膀胱切除术以及切除雷济厄斯间隙和脐部的组织。然而，结果令人失望，因为大多数资料中的五年生存率不超过10%。放疗的价值存疑，化疗在治疗中几乎没有价值。
