特纳综合征中的左心发育不全：移植的主要指征？
Hypoplastic left heart in Turner's syndrome: a primary indication for transplant?
作者信息
Philip Joseph, Gupta Dipankar, Bleiweis Mark S, Pietra Biagio A, Vyas Himesh V
机构信息
Congenital Heart Center,UF Health Shands Children's Hospital,University of Florida,Gainesville,Florida,United States of America.
出版信息
Cardiol Young. 2018 Mar;28(3):458-460. doi: 10.1017/S1047951117001962. Epub 2017 Dec 13.
Survival for hypoplastic left heart syndrome patients following the Norwood procedure is 71-90%. Mortality in patients with Turner's syndrome and hypoplastic left heart syndrome after conventional palliation (Norwood operation) has been reported as high as 80%. This questions the approach of traditional staged palliation. Here, we report a patient with hypoplastic left heart syndrome and Turner's syndrome bridged to orthotopic heart transplantation following a hybrid procedure.
诺伍德手术后，左心发育不全综合征患者的生存率为71%-90%。据报道，患有特纳综合征和左心发育不全综合征的患者在进行传统姑息治疗（诺伍德手术）后的死亡率高达80%。这对传统分期姑息治疗方法提出了质疑。在此，我们报告一例患有左心发育不全综合征和特纳综合征的患者，在接受杂交手术后成功过渡到原位心脏移植。
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