1Department of Medicine (Neurology),University of Ottawa,Ottawa,Ontario,Canada.
4Division of Nuclear Medicine,The Ottawa Hospital,Ottawa,Ontario,Canada.
Can J Neurol Sci. 2018 Mar;45(2):137-143. doi: 10.1017/cjn.2017.282. Epub 2018 Jan 8.
Neurolymphomatosis is a process of neoplastic endoneurial invasion, most strongly associated with non-Hodgkin's lymphoma. It must be distinguished from paraneoplastic, metabolic, nutritional and treatment-related causes of neuropathy that are common in this patient population.
This brief case series illustrates the protean manifestations of neurolymphomatosis of the brachial plexus, ranging from focal distal mononeuropathy to multifocal brachial plexopathy, either as the index manifestation of lymphoma or as a complication of relapsing disease.
Prominent asymmetry, pain and nodular involvement on neuroimaging may help distinguish neurolymphomatosis from paraneoplastic immune demyelinating radiculoneuropathy. MR neurography criteria for the diagnosis of neurolymphomatosis include hyperintensity on T2 and STIR sequences, focal and diffuse nerve enlargement with fascicular disorganization and gadolinium enhancement. No specific anatomical distribution within the brachial plexus has, however, been found to be characteristic. Fluorodeoxyglucose-positron emission tomography (FDG-PET) imaging is the imaging modality with the highest sensitivity for detection of nodal or extranodal spread in lymphoma.
Brachial plexus neuropathy in neurolymphomatosis is highly protean in its distribution, semiology and relation to lymphoma staging. Dedicated MRI and PET-CT imaging are leading diagnostic modalities.
神经淋巴瘤病是一种肿瘤性神经内膜侵袭过程,与非霍奇金淋巴瘤关系最为密切。必须将其与常见于此类患者人群的神经病变的副瘤、代谢、营养和治疗相关原因相区分。
本简要病例系列说明了臂丛神经淋巴瘤病的多种表现形式,从局灶性远端单神经病到多灶性臂丛神经病,无论是作为淋巴瘤的首发表现还是作为复发性疾病的并发症。
神经影像学上明显的不对称、疼痛和结节性受累可能有助于将神经淋巴瘤病与副瘤性免疫脱髓鞘神经根神经病区分开来。神经淋巴瘤病的磁共振神经成像诊断标准包括 T2 和短回波序列的高信号、局灶性和弥漫性神经肿大伴束状结构紊乱和钆增强。然而,尚未发现臂丛内的特定解剖分布具有特征性。氟脱氧葡萄糖正电子发射断层扫描(FDG-PET)成像在检测淋巴瘤的淋巴结或结外扩散方面具有最高的灵敏度。
神经淋巴瘤病中的臂丛神经病变在分布、症状学和与淋巴瘤分期的关系方面具有高度的多样性。专门的 MRI 和 PET-CT 成像为主要的诊断方式。