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挥发性麻醉用于极长链酰基辅酶A脱氢酶缺乏症患儿:一例报告

Volatile anesthesia for a pediatric patient with very long-chain acyl-coenzyme A dehydrogenase deficiency: A case report.

作者信息

Hess Aaron S, Rice Gregory M, Jochman John D, Muldowney Bridget L

机构信息

Department of Anesthesiology, University of Wisconsin Hospital and Clinics, Madison, WI, USA.

Department of Pediatrics, University of Wisconsin Hospital and Clinics, Madison, WI, USA.

出版信息

Paediatr Anaesth. 2018 Mar;28(3):296-297. doi: 10.1111/pan.13314. Epub 2018 Jan 9.

DOI:10.1111/pan.13314
PMID:29316010
Abstract

We report the case of a 3-year-old boy with very long-chain acyl-coenzyme A dehydrogenase deficiency presenting for adenotonsillectomy who was successfully and safely managed with a balanced anesthetic including sevoflurane. The anesthetic management is described, and the controversy surrounding volatile anesthetics in these patients is discussed.

摘要

我们报告了一例3岁患有极长链酰基辅酶A脱氢酶缺乏症的男孩,因腺样体扁桃体切除术前来就诊,其通过包括七氟醚在内的平衡麻醉得以成功且安全地进行管理。文中描述了麻醉管理情况,并讨论了这些患者中关于挥发性麻醉剂的争议。

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Anesthetic Management and Neuromonitoring in a Patient with Very Long-Chain Acyl-Coenzyme A Dehydrogenase Deficiency Undergoing Scoliosis Surgery: A Case Report and Review of Literature.极长链酰基辅酶A脱氢酶缺乏症患者行脊柱侧弯手术的麻醉管理与神经监测:一例报告及文献复习
Case Rep Anesthesiol. 2024 Jan 8;2024:1050279. doi: 10.1155/2024/1050279. eCollection 2024.
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The perioperative transition of serum biomarkers of a 1.5-year-old boy with very-long-chain acyl-CoA dehydrogenase deficiency.一名患有极长链酰基辅酶A脱氢酶缺乏症的1.5岁男孩围手术期血清生物标志物的变化
Mol Genet Metab Rep. 2021 Apr 19;27:100760. doi: 10.1016/j.ymgmr.2021.100760. eCollection 2021 Jun.