León Rachel L, Zaban Nicholas B, Schamberger Marcus S, Ho Chang Y, Mietzsch Ulrike
Division of Neonatology, Department of Pediatrics, Indiana University School of Medicine, Indianapolis, IN, USA.
Neonatology. 2018;113(3):231-234. doi: 10.1159/000485829. Epub 2018 Jan 10.
Small remnants of the right valve of the sinus venosus are commonly found in adults, but the incidence and risk associated with these embryonic remnants in neonates are not well studied. The following report describes a cyanotic neonate with a large Eustachian valve remnant creating a functional cor triatriatum dexter who was initially diagnosed with persistent pulmonary hypertension of the newborn. The cyanosis in this infant improved over the first postnatal week with conservative management, but she suffered multifocal subcortical stroke, likely related to her intracardiac shunt. The clinical presentation and questions regarding long-term management of this rare diagnosis are explored.
成人中常见静脉窦右瓣的小残余，但这些胚胎残余在新生儿中的发生率及相关风险尚未得到充分研究。以下报告描述了一名患有巨大欧氏瓣残余的青紫新生儿，该残余导致功能性右三房心，最初被诊断为新生儿持续性肺动脉高压。该婴儿的青紫在出生后的第一周通过保守治疗有所改善，但她发生了多灶性皮质下中风，可能与心内分流有关。本文探讨了这种罕见诊断的临床表现及长期管理问题。
