Çetin Güvenç Rengin, Akgün Gökmen, Güvenç Tolga S
1Department of Cardiology,Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital,Istanbul,Turkey.
2Department of Pediatric Cardiology,Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital,Istanbul,Turkey.
Cardiol Young. 2018 Apr;28(4):608-610. doi: 10.1017/S1047951117002712. Epub 2018 Jan 10.
Ebstein's anomaly is a rare CHD that is characterised by caudal displacement of the functional tricuspid annulus and a dysfunctional tricuspid valve owing to a failure of proper leaflet coaptation. We present a balanced variant of Ebstein's anomaly, in which the overgrowth of the septal leaflet had allowed proper coaptation of the tricuspid leaflets, thus preserving the valve function.
埃布斯坦畸形是一种罕见的先天性心脏病,其特征是功能性三尖瓣环尾端移位以及由于瓣叶不能正常对合导致三尖瓣功能障碍。我们展示了埃布斯坦畸形的一种平衡变异型,其中隔叶过度生长使得三尖瓣叶能够正常对合,从而保留了瓣膜功能。