Emge Drew A, Lewis Daniel J, Aung Phyu P, Duvic Madeleine
1 Department of Internal Medicine, Baylor College of Medicine, Houston, TX, USA.
2 School of Medicine, Baylor College of Medicine, Houston, TX, USA.
J Cutan Med Surg. 2018 May/Jun;22(3):336-340. doi: 10.1177/1203475417752366. Epub 2018 Jan 10.
Folliculotropic mycosis fungoides (FMF) is a variant of mycosis fungoides (MF) with folliculotropic, atypical lymphocytes that may or may not have mucin deposition surrounding the hair follicle. Follicular mucinosis (FM) is a primary or secondary finding in FMF, lupus, or collagen vascular diseases that is only a histological process of mucin deposition surrounding the hair follicles. We present a case of a 6-year-old boy who had features of both FMF and primary follicular mucinosis (PFM). The case reveals key insights on FMF with concurrent FM in pediatric patients and how to differentiate between FMF and PFM.
亲毛囊性蕈样肉芽肿(FMF)是蕈样肉芽肿(MF)的一种变体,具有亲毛囊性非典型淋巴细胞,这些淋巴细胞可能有也可能没有围绕毛囊的粘蛋白沉积。毛囊粘蛋白病(FM)是FMF、狼疮或胶原血管疾病中的一种原发性或继发性表现,它仅仅是围绕毛囊的粘蛋白沉积的组织学过程。我们报告一例6岁男孩,其具有FMF和原发性毛囊粘蛋白病(PFM)的特征。该病例揭示了小儿患者中FMF合并FM的关键见解以及如何区分FMF和PFM。