Department of Pediatric Cardiology, Fortis-ESCORT Heart Institute, New Delhi, India.
Department of Pediatric Cardiac Surgery, Fortis-ESCORT Heart Institute, New Delhi, India.
World J Pediatr Congenit Heart Surg. 2020 Jul;11(4):NP113-NP116. doi: 10.1177/2150135117743224. Epub 2018 Jan 15.
A supramitral ring is a rare cause of mitral stenosis, while an isolated mitral valve cleft is a rare cause of congenital mitral regurgitation. Fortunately, both the lesions are known to have good outcomes after surgical correction. Although each is known to be associated with a variety of other structural heart defects, their coexistence has not been reported previously. We report a case of a three- and half-year-old boy detected to have a rare combination of supramitral ring producing severe mitral stenosis with a coexisting cleft in the anterior leaflet of mitral valve causing severe mitral regurgitation. The patient underwent successful surgical repair with resolution of both mitral stenosis and regurgitation.
瓣上环是二尖瓣狭窄的罕见病因,而单纯性二尖瓣裂则是先天性二尖瓣反流的罕见病因。幸运的是,这两种病变在手术后都有良好的结果。虽然已知这两种病变都与多种其他结构性心脏缺陷有关,但它们同时存在以前尚未有报道。我们报告了一例三岁半男孩,发现罕见的瓣上环合并二尖瓣前叶裂导致严重二尖瓣反流,导致严重二尖瓣狭窄。患者成功接受了手术修复,二尖瓣狭窄和反流均得到解决。