• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

Recombinant ADAMTS 13 in thrombotic thrombocytopenic purpura.

作者信息

Scully Marie, Hibbard Christopher, Ewenstein Bruce

机构信息

Department of Haemotology; University College London Hospitals NHS Trust, Cardiometabolic Programme-NHR UCLH/UCL BRC, London, UK.

出版信息

Oncoscience. 2017 Nov 28;4(11-12):160-161. doi: 10.18632/oncoscience.380. eCollection 2017 Nov.

DOI:10.18632/oncoscience.380
PMID:29344548
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5769974/
Abstract
摘要

相似文献

1
Recombinant ADAMTS 13 in thrombotic thrombocytopenic purpura.重组ADAMTS 13在血栓性血小板减少性紫癜中的应用
Oncoscience. 2017 Nov 28;4(11-12):160-161. doi: 10.18632/oncoscience.380. eCollection 2017 Nov.
2
Preclinical assessment of a new recombinant ADAMTS-13 drug product (BAX930) for the treatment of thrombotic thrombocytopenic purpura.新型重组 ADAMTS-13 药物(BAX930)治疗血栓性血小板减少性紫癜的临床前评估。
J Thromb Haemost. 2016 Jul;14(7):1410-9. doi: 10.1111/jth.13341. Epub 2016 Jul 2.
3
Pharmacokinetics of plasma infusion in congenital thrombotic thrombocytopenic purpura.血浆输注在先天性血栓性血小板减少性紫癜中的药代动力学。
J Thromb Haemost. 2019 Jan;17(1):88-98. doi: 10.1111/jth.14345. Epub 2018 Dec 31.
4
High prevalence of hereditary thrombotic thrombocytopenic purpura in central Norway: from clinical observation to evidence.挪威中部遗传性血栓性血小板减少性紫癜的高发率:从临床观察到证据。
J Thromb Haemost. 2016 Jan;14(1):73-82. doi: 10.1111/jth.13186. Epub 2016 Jan 8.
5
Platelet rescue by macrophage depletion in obese ADAMTS-13-deficient mice at risk of thrombotic thrombocytopenic purpura.肥胖型 ADAMTS-13 缺乏症小鼠中巨噬细胞耗竭对血栓性血小板减少性紫癜风险的血小板保护作用。
J Thromb Haemost. 2018 Jan;16(1):150-163. doi: 10.1111/jth.13901. Epub 2017 Nov 28.
6
Targeted ADAMTS-13 replacement therapy for thrombotic thrombocytopenic purpura.针对血栓性血小板减少性紫癜的靶向 ADAMTS-13 替代治疗。
J Thromb Haemost. 2024 Apr;22(4):896-904. doi: 10.1016/j.jtha.2023.11.030. Epub 2023 Dec 22.
7
Prevalence of the ADAMTS-13 missense mutation R1060W in late onset adult thrombotic thrombocytopenic purpura.成人晚发型血栓性血小板减少性紫癜中ADAMTS-13错义突变R1060W的患病率
J Thromb Haemost. 2008 Feb;6(2):331-8. doi: 10.1111/j.1538-7836.2008.02846.x. Epub 2007 Nov 20.
8
Prevention of relapse in patients with acquired thrombotic thrombocytopenic purpura undergoing elective surgery: a case series.获得性血栓性血小板减少性紫癜患者择期手术预防复发:病例系列研究。
J Thromb Haemost. 2019 Mar;17(3):492-498. doi: 10.1111/jth.14381. Epub 2019 Feb 25.
9
ADAMTS-13 antigen and activity levels in thrombocytopenic disorders including thrombotic thrombocytopenic purpura in Kuwait.在科威特,包括血栓性血小板减少性紫癜在内的血小板减少性疾病中 ADAMTS-13 抗原和活性水平。
Acta Haematol. 2011;125(3):160-6. doi: 10.1159/000322391. Epub 2010 Dec 24.
10
Preventative and therapeutic effects of a novel humanized anti-glycoprotein Ibα fragment of antigen-binding region in a murine model of thrombotic thrombocytopenic purpura.新型抗原结合区人源化抗糖蛋白Ibα片段在血栓性血小板减少性紫癜小鼠模型中的预防和治疗作用
J Thromb Haemost. 2025 May;23(5):1596-1607. doi: 10.1016/j.jtha.2025.02.009. Epub 2025 Feb 15.

引用本文的文献

1
ADAMTS13 Improves Hepatic Platelet Accumulation in Pyrrolizidine Alkaloids-induced Liver Injury.ADAMTS13改善吡咯里西啶生物碱诱导的肝损伤中的肝血小板聚集。
J Clin Transl Hepatol. 2025 Jan 28;13(1):25-34. doi: 10.14218/JCTH.2024.00233. Epub 2024 Nov 22.
2
Apadamtase Alfa: First Approval.阿达马塔酶α:首次获批。
Drugs. 2024 Apr;84(4):467-472. doi: 10.1007/s40265-024-02007-6.
3
Sepsis-Pathophysiology and Therapeutic Concepts.脓毒症——病理生理学与治疗理念
Front Med (Lausanne). 2021 May 14;8:628302. doi: 10.3389/fmed.2021.628302. eCollection 2021.
4
Hereditary thrombotic thrombocytopenic purpura.遗传性血栓性血小板减少性紫癜
Haematologica. 2019 Oct;104(10):1916-1918. doi: 10.3324/haematol.2019.225896.
5
ADAMTS proteins in human disorders.人类疾病中的 ADAMTS 蛋白。
Matrix Biol. 2018 Oct;71-72:225-239. doi: 10.1016/j.matbio.2018.06.002. Epub 2018 Jun 6.

本文引用的文献

1
The role of ADAMTS13 in acute myocardial infarction: cause or consequence?ADAMTS13在急性心肌梗死中的作用:原因还是结果?
Cardiovasc Res. 2016 Aug 1;111(3):194-203. doi: 10.1093/cvr/cvw097. Epub 2016 May 12.
2
ADAMTS13-mediated thrombolysis of t-PA-resistant occlusions in ischemic stroke in mice.ADAMTS13 介导的溶栓治疗对缺血性脑卒中 t-PA 抵抗性闭塞的作用。
Blood. 2016 May 12;127(19):2337-45. doi: 10.1182/blood-2015-08-662650. Epub 2016 Feb 29.
3
Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura.ADAMTS基因家族成员的突变会导致血栓性血小板减少性紫癜。
Nature. 2001 Oct 4;413(6855):488-94. doi: 10.1038/35097008.
4
Recovery and half-life of von Willebrand factor-cleaving protease after plasma therapy in patients with thrombotic thrombocytopenic purpura.血栓性血小板减少性紫癜患者血浆治疗后血管性血友病因子裂解蛋白酶的恢复情况及半衰期
Thromb Haemost. 1999 Jan;81(1):8-13.
5
Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura.急性血栓性血小板减少性紫癜中针对血管性血友病因子裂解蛋白酶的抗体。
N Engl J Med. 1998 Nov 26;339(22):1585-94. doi: 10.1056/NEJM199811263392203.
6
Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura.慢性复发性血栓性血小板减少性紫癜中血管性血友病因子裂解蛋白酶活性缺乏
Blood. 1997 May 1;89(9):3097-103.