Knight J A, Wilson J F
Pediatr Pathol. 1985;4(1-2):13-23. doi: 10.3109/15513818509025899.
We report 2 cases of primary pulmonary hypertension in brothers, 6 and 3 years old. Their lungs contained numerous plexiform vascular lesions. The literature is reviewed involving familial cases, especially those in which siblings were affected. Several of these cases lack the pathological verification necessary for acceptance as examples of plexogenic pulmonary arteriopathy.
我们报告了2例原发性肺动脉高压病例,患者为6岁和3岁的兄弟俩。他们的肺部有大量丛状血管病变。本文回顾了相关文献,涉及家族性病例,尤其是兄弟姐妹受影响的病例。其中一些病例缺乏作为丛发性肺动脉病实例所必需的病理证实。