Department of Radiology, Ghent University Hospital, De Pintelaan 185, 9000 Ghent, Belgium.
Postgraduation School in Radiodiagnostics, Università degli Studi di Milano, Via Festa del Perdono, 7, 20122 Milano, MI, Italy.
Future Oncol. 2018 Dec;14(28):2923-2931. doi: 10.2217/fon-2017-0649. Epub 2018 Jan 29.
Primary retroperitoneal mucinous cystadenoma (PRMC) is an extremely rare tumor: its histogenesis and its biological behavior remain speculative. Since most retroperitoneal tumors are malignant, a preoperative diagnosis of benignity is essential and it can be reached through imaging examinations, allowing a conservative management approach. We describe the case of a 52-year-old woman with abdominal pain and a palpable mass. Computed tomography of the abdomen revealed a retroperitoneal cystic mass, which was resected successfully through laparoscopy and diagnosed as PRMC. Although there are no pathognomonic, clinical or radiological findings for PRMC, it should be included in the list of differential diagnoses and its imaging criteria of benignity should always be sought, with the aim to exclude malignant tumors.
原发性腹膜后黏液囊腺瘤(PRMC)是一种极其罕见的肿瘤:其组织发生和生物学行为仍存在推测。由于大多数腹膜后肿瘤为恶性,因此术前诊断的良性至关重要,这可以通过影像学检查来实现,从而采取保守的管理方法。我们描述了一位 52 岁女性患者,其主要表现为腹痛和可触及的肿块。腹部计算机断层扫描显示为腹膜后囊性肿块,通过腹腔镜成功切除,并诊断为 PRMC。尽管 PRMC 没有特异性的临床或影像学表现,但仍应将其纳入鉴别诊断列表,并始终寻求其良性的影像学标准,以排除恶性肿瘤。