Mier Escurra Erik Antonio, Díaz Prieto Talia, Fernández Ortíz Sergio Javier, Mier Saad Guillermo, Valdes Cepeda Alejandro
Programa Multicéntrico de la Especialidad Médica de Pediatría de la Escuela de Medicina, Tecnológico de Monterrey, Secretaria de Salud de Nuevo León, Monterrey, México.
Programa Multicéntrico de la Especialidad Médica de Pediatría de la Escuela de Medicina, Tecnológico de Monterrey, Secretaria de Salud de Nuevo León, Monterrey, México.
Bol Med Hosp Infant Mex. 2016 Jul-Aug;73(4):250-255. doi: 10.1016/j.bmhimx.2016.04.003. Epub 2016 Aug 1.
Acute colonic pseudo-obstruction, also known as Ogilvie syndrome, is a rare gastrointestinal syndrome in children. It is characterized by a marked dilatation of the colon evidenced by imaging and absence of mechanical obstruction. Patients typically present with abdominal pain and distended, tympanic abdomen, with peristalsis present, accompanied by nausea and vomiting. Up to 40% of patients can pass gas and/or have bowel movements. We decide to report this case because this syndrome is very rare in pediatric patients, and no cases have been reported in a post-renal transplant pediatric patient.
13 year old male patient with past medical history of psychomotor retardation due to perinatal asphyxia and chronic renal failure secondary to bilateral renal hypoplasia. Treated with peritoneal dialysis for one year until kidney transplant was performed. Currently under immunosuppressive regime. He began his condition with mild abdominal pain accompanied by semi-liquid stools, and progressive distention up to 78cm of abdominal circumference in 72hours, so image studies were performed. Managed with prokinetic drugs without any improvement. Two exploratory laparotomies observed flanges, without evidence of any mechanical obstruction. An abdominal magnetic resonance was performed, where important intestinal dilatation was observed with no evidence of mechanical obstruction. Ogilvie Syndrome was diagnosed, so management with neostigmine was established, which led to symptom resolution.
This case is reported because this syndrome is very rare in children, there is little clinical suspicion and lack of management guides for diagnosis and treatment in patients of this age.
急性结肠假性梗阻,又称奥吉尔维综合征,是儿童中一种罕见的胃肠综合征。其特征为影像学显示结肠显著扩张且无机械性梗阻。患者通常表现为腹痛、腹部膨隆呈鼓音,有蠕动,伴有恶心和呕吐。高达40%的患者可排气和/或排便。我们决定报告此病例,因为该综合征在儿科患者中非常罕见,且肾移植术后儿科患者中尚无病例报告。
一名13岁男性患者,有围产期窒息所致精神运动发育迟缓及双侧肾发育不全继发慢性肾衰竭的既往病史。接受腹膜透析治疗一年,直至进行肾移植。目前处于免疫抑制状态。他起初出现轻度腹痛并伴有稀便,72小时内腹围逐渐增大至78厘米,因此进行了影像学检查。使用促动力药物治疗无任何改善。两次剖腹探查均观察到肠襻,无任何机械性梗阻的证据。进行了腹部磁共振成像检查,观察到肠道明显扩张且无机械性梗阻证据。诊断为奥吉尔维综合征,因此采用新斯的明治疗,症状得以缓解。
报告此病例是因为该综合征在儿童中非常罕见,临床怀疑较少,且该年龄段患者缺乏诊断和治疗的管理指南。