Guttadauro Angelo, Maternini Matteo, Frassani Silvia, Guanziroli Elena, Lo Bianco Giulia, Gabrielli Francesco
Ann Ital Chir. 2017 Nov 20;6:S2239253X17027840.
Desmoid tumor is a rare soft tissues neoplasia characterized by local invasiveness and by a tendency towards local recurrence although not towards metastasization.
Etiology is not clear. Desmoid tumors originate from the monoclonal proliferation of one mesenchymal cell and develop in the context of fascial, muscular and aponeurotic tissue. They are free of capsule and do not usually metastatize, although they do present a high risk of local recurrence CONCLUSION: In the absence of a systematic data collection and of a clear distinction, in the existing databases, between primitive and recurrent lesions and between lesions of different sites, there are no standard guidelines for a correct management of desmoids.
Aggressive fibromatos Desmoid tumor, Soft tissue neoplasia.
硬纤维瘤是一种罕见的软组织肿瘤,其特征是具有局部侵袭性且有局部复发倾向,但无转移倾向。
病因尚不清楚。硬纤维瘤起源于单个间充质细胞的单克隆增殖,发生于筋膜、肌肉和腱膜组织中。它们无包膜,通常不转移,尽管存在较高的局部复发风险。结论:由于缺乏系统的数据收集,且现有数据库中未对原发性和复发性病变以及不同部位的病变进行明确区分,因此对于硬纤维瘤的正确管理尚无标准指南。
侵袭性纤维瘤病;硬纤维瘤;软组织肿瘤