Sabba Marcelo Ferreira, Renor Beatriz Souza, Ghizoni Enrico, Tedeschi Helder, Joaquim Andrei Fernandes
MD. Neurosurgery Resident, Universidade Estadual de Campinas (Unicamp), Campinas, SP, Brazil.
MD, PhD. Professor of Neurosurgery, Unicamp, Campinas, SP, Brazil.
Rev Assoc Med Bras (1992). 2017 Nov;63(11):946-949. doi: 10.1590/1806-9282.63.11.946.
Chiari malformation (CM) is the most common and prevalent symptomatic congenital craniocervical malformation. Radiological diagnosis is established when the cerebellar tonsils are located 5 mm or more below the level of the foramen magnum on magnetic resonance imaging (MRI). Surgical treatment is indicated whenever there is symptomatic tonsillar herniation or syringomyelia/hydrocephalus. The main surgical treatment for CM without craniocervical instability (such as atlantoaxial luxation) is posterior fossa decompression, with or without duraplasty. The authors describe in details and in a stepwise fashion the surgical approach of patients with CM as performed at the State University of Campinas, emphasizing technical nuances for minimizing the risks of the procedure and potentially improving patient outcome.
Chiari畸形(CM)是最常见且普遍存在的有症状的先天性颅颈交界区畸形。当磁共振成像(MRI)显示小脑扁桃体位于枕骨大孔水平以下5毫米或更低时,即可确立影像学诊断。只要存在有症状的扁桃体疝或脊髓空洞症/脑积水,就应进行手术治疗。对于没有颅颈交界区不稳定(如寰枢椎脱位)的CM,主要的手术治疗方法是后颅窝减压术,可伴或不伴硬脑膜成形术。作者详细且逐步地描述了坎皮纳斯州立大学对CM患者所采用的手术方法,强调了技术细节,以尽量降低手术风险并可能改善患者预后。