Suffredini Giancarlo, Diaz-Rodriguez Natalia, Chakravarthy Krishnan, Mathur Aarti, Hayanga Heather K, Frank Steve M, Ringel Richard E, Freiberg Stephen, Barodka Viachaslau M, Steppan Jochen
Anesthesiology and Critical Care Medicine, The Johns Hopkins University School of Medicine.
Anesthesia and Critical Care Medicine, The Johns Hopkins University School of Medicine.
Cureus. 2017 Dec 8;9(12):e1928. doi: 10.7759/cureus.1928.
Survival rates for patients with palliated congenital heart disease are increasing, and an increasing number of adults with cyanotic congenital heart disease (CCHD) might require surgical resection of pheochromocytoma-paraganglioma (PHEO-PGL). A recent study supports the idea that patients with a history of CCHD and current or historical cyanosis might be at increased risk for developing PHEO-PGL. We review the anesthetic management of two adults with single-ventricle physiology following Fontan palliation presenting for PHEO-PGL resection and review prior published case reports. We found the use of epidural analgesia to be safe and effective in the operative and postoperative management of our patients.
姑息性先天性心脏病患者的生存率正在提高，越来越多患有青紫型先天性心脏病（CCHD）的成年人可能需要手术切除嗜铬细胞瘤-副神经节瘤（PHEO-PGL）。最近的一项研究支持这样的观点，即有CCHD病史且目前或既往有青紫的患者发生PHEO-PGL的风险可能增加。我们回顾了两名接受Fontan姑息治疗后具有单心室生理的成年人因PHEO-PGL切除而进行的麻醉管理，并回顾了先前发表的病例报告。我们发现，在我们患者的手术和术后管理中使用硬膜外镇痛是安全有效的。
