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FDG PET/CT 在监测家族性噬血细胞性淋巴组织细胞增生症疾病活动度方面有何潜力?

Is There Any Potential of FDG PET/CT in Monitoring Disease Activity in Familial Hemophagocytic Lymphohistiocytosis?

机构信息

From the PET Center, XiangYa Hospital, Central South University, Changsha, China.

出版信息

Clin Nucl Med. 2018 Apr;43(4):296-298. doi: 10.1097/RLU.0000000000002008.

DOI:10.1097/RLU.0000000000002008
PMID:29465491
Abstract

FDG PET/CT was performed in a 30-year-old woman to detect the source of fever of unknown origin. The images showed widespread abnormal activity, consistent with lymphoma. However, lymph node biopsy revealed only inflammation, and a diagnosis of familial hemophagocytic lymphohistiocytosis was eventually made after familial hemophagocytic lymphohistiocytosis-specific gene was detected. After proper therapy, a follow-up FDG PET/CT examination 2 months later showed resolution of most of the previously seen lesions.

摘要

一位 30 岁女性因不明原因发热行 FDG PET/CT 检查,结果显示广泛的异常活性,符合淋巴瘤。然而,淋巴结活检仅显示炎症,在检测到家族性噬血细胞性淋巴组织细胞增多症特异性基因后,最终诊断为家族性噬血细胞性淋巴组织细胞增多症。经过适当治疗,2 个月后复查 FDG PET/CT 显示大部分先前发现的病灶已消退。

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Front Med (Lausanne). 2021 Dec 22;8:792677. doi: 10.3389/fmed.2021.792677. eCollection 2021.