Mota Fernando, Horta Miguel, Marques Claudia, Foreid Susan, Selores Manuela
Dermatology Department, Centro Hospitalar do Porto, Portugal.
Dermatol Online J. 2017 Oct 15;23(10):13030/qt6ff381x4.
Extramammary Paget disease of the vulva is a rare condition that accounts for only 1-2% of vulvar malignancies and represents a frequent cause of misdiagnosis. It is most commonly seen in postmenopausal women. Clinically it is similar to Paget disease of the breast, appearing as red, well-demarcated eczematoid lesions, with slightly raised edges. A high degree of clinical suspicion is very important when evaluating these lesions in order to avoid misdiagnosis and delay of effective treatment. We present a case of vulvar Paget disease treated with vulvectomy.
外阴部乳房外佩吉特病是一种罕见疾病，仅占外阴恶性肿瘤的1%-2%，且是误诊的常见原因。它最常见于绝经后女性。临床上它与乳腺佩吉特病相似，表现为边界清晰的红色湿疹样病变，边缘略有隆起。在评估这些病变时，高度的临床怀疑非常重要，以避免误诊和有效治疗的延迟。我们报告一例接受外阴切除术治疗的外阴佩吉特病病例。
