Department of Neurology, The Second Affiliated Hospital of Nanchang University, Nanchang, Jiangxi, 330006, China.
Neurol Sci. 2018 Jul;39(7):1293-1296. doi: 10.1007/s10072-018-3292-7. Epub 2018 Feb 26.
Intracranial dural arteriovenous fistulas (DAVFs), constituting approximately 10 to15% of intracranial vascular malformations, are anomalous direct connections between dural arteries and venous sinuses, meningeal veins, or cortical veins; the arterial feeders are various, usually fed by branches of internal carotid, external carotid, or vertebral artery (Santillan et al. CNN 115(3):241-251, 2013; Holoekamp et al. JN 124(6):1752-65, 2016; Terada T et al. JN 80(5):884-9, 1994). Spectrums of clinical presentations are widespread, arranging from pulsatile tinnitus to intracranial hemorrhage. Such DAVFs with rapidly progressive dementia as primary presentation, which has been reported in several literature, are still extremely scarce (Santillan et al. CNN 115(3):241-251, 2013; Holoekamp et al JN 124(6):1752-65, 2016). Up to 2015, similar reports are less than 20 cases (Holoekamp et al. JN 124(6):1752-65, 2016). Herein, we report a patient who was misdiagnosed with encephalitis, presented thalamic dementia, and was ultimately diagnosed of DAVFs.
颅内硬脑膜动静脉瘘（DAVF）约占颅内血管畸形的 10%至 15%，是硬脑膜动脉和静脉窦、脑膜静脉或皮质静脉之间异常的直接连接；动脉供血者多种多样，通常由颈内动脉、颈外动脉或椎动脉的分支供血（Santillan 等人，CNN 115(3):241-251, 2013；Holoekamp 等人，JN 124(6):1752-65, 2016；Terada T 等人，JN 80(5):884-9, 1994）。临床表现广泛，从搏动性耳鸣到颅内出血不等。有文献报道，以迅速进展性痴呆为主要表现的此类 DAVF 仍极为罕见（Santillan 等人，CNN 115(3):241-251, 2013；Holoekamp 等人，JN 124(6):1752-65, 2016）。截至 2015 年，类似的报道不到 20 例（Holoekamp 等人，JN 124(6):1752-65, 2016）。在此，我们报告了 1 例误诊为脑炎、表现为丘脑性痴呆、最终诊断为 DAVF 的患者。
