Department of Hepatobiliary and Pancreatic Surgery, Bethune Hospital 1, Changchun, Jilin, 130021, China.
World J Surg Oncol. 2018 Mar 5;16(1):43. doi: 10.1186/s12957-018-1326-5.
Adrenocortical carcinoma (ACC) is a rare, heterogeneous malignancy with a poor prognosis. ACCs are classified as functioning and non-functioning. The pathogenesis of ACC remains elusive, and diagnosis of ACC is currently based on pathology. In the absence of other effective approaches, surgical resection is the preferred treatment option.
Here, we report a case of ACC in the retroperitoneum. The patient underwent radical adrenalectomy and remained disease-free throughout a 6-month follow-up.
Radical surgical resection is an efficient therapy for ACC, and hydrocortisone can be used to alleviate symptoms of secondary acute adrenal hypofunction.
肾上腺皮质癌(adrenocortical carcinoma,ACC)是一种罕见的、异质性的恶性肿瘤,预后不良。ACC 分为功能性和非功能性。ACC 的发病机制仍不清楚,目前 ACC 的诊断基于病理学。在缺乏其他有效方法的情况下,手术切除是首选的治疗方法。
我们在此报告一例腹膜后 ACC 病例。患者接受了根治性肾上腺切除术,在 6 个月的随访期间无疾病复发。
根治性手术切除是 ACC 的有效治疗方法,氢化可的松可用于缓解继发急性肾上腺功能减退的症状。