Monroig-Bosque Paloma Del C, Okoye Ekene I
Department of Pathology and Genomic Medicine, Houston Methodist Hospital, Houston, TX.
Department of Pathology and Genomic Medicine, Houston Methodist Hospital, Houston, TX
Ann Clin Lab Sci. 2018 Jan;48(1):116-119.
Mullerian duct anomalies (MDAs) are congenital defects of the female genital system that arise from abnormal embryological development of the Mullerian ducts. Septate uterus is the most common, resulting from incomplete resorption of the medial septum after fusion of the Mullerian ducts. Two main types of septate uterus exist, including septa that extend completely or partially from the uterine fundus to the cervical os. The combination of a uterine septum with a double cervix has been previously described; however, in most cases the septum was complete. We present a case of a 23-year-old female with a partial uterine septum and a double cervix. We refer to this atypical MDA as "uterus septus subtotalis bicollis". The description, characterization, and diagnosis of rare MDAs is important as they imply distinct therapeutic modalities.
苗勒管异常（MDA）是女性生殖系统的先天性缺陷，由苗勒管胚胎发育异常引起。纵隔子宫最为常见，是由于苗勒管融合后内侧纵隔未完全吸收所致。纵隔子宫主要有两种类型，包括从子宫底延伸至宫颈内口的完全或部分纵隔。子宫纵隔合并双宫颈的情况此前已有描述；然而，在大多数情况下纵隔是完整的。我们报告一例23岁女性，患有部分子宫纵隔和双宫颈。我们将这种非典型的MDA称为“部分纵隔双宫颈子宫”。罕见MDA的描述、特征及诊断很重要，因为它们意味着不同的治疗方式。
