表现为急性阴囊的卵睾性发育障碍

Ovotesticular Disorder of Sex Development Presenting as an Acute Scrotum.

作者信息

Mirshahvalad Seyed Ali, Alinia Paria, Hekmati Pooya, Nafisi Nahid, Kajbafzadeh Abdol-Mohammad

机构信息

Pediatric Urology and Regenerative Medicine Research Center, Section of Tissue Engineering and Stem Cells Therapy, Children's Hospital Medical Center, Tehran University of Medical Sciences, Tehran, Iran.

Iran University of Medical Science, RasoleAkram Hospital, Tehran, Islamic Republic of Iran.

出版信息

Urology. 2018 Jun;116:176-179. doi: 10.1016/j.urology.2017.12.025. Epub 2018 Mar 13.

DOI:10.1016/j.urology.2017.12.025

PMID:29548867

Abstract

Hermaphroditism is known as ovotesticular disorder of sex development. A 14-year-old boy was admitted with right acute scrotum. Exploration revealed tunica rupture and hematoma, with no viable tissue. After 1 month, he was admitted again with left hemiscrotal pain. Microscopic examination of the left gonad demonstrated foci of hemorrhagic cysts, primordial follicles, and regions of seminiferous tubules. We preserved a testicular tissue and the ovarian part was extracted completely. Long-term follow-up with his hormonal profile is reported. This is a case of ovotesticular disorder presented with acute scrotum and we also tried to reduce long-term hormone therapy, with preservation of testicular part.

摘要

两性畸形被称为性发育的卵睾体障碍。一名14岁男孩因右侧急性阴囊入院。探查发现白膜破裂和血肿，无存活组织。1个月后，他因左侧阴囊疼痛再次入院。对左侧性腺的显微镜检查显示有出血性囊肿灶、原始卵泡和生精小管区域。我们保留了一块睾丸组织，并将卵巢部分完全切除。报告了对其激素水平的长期随访情况。这是一例以急性阴囊表现的卵睾体障碍病例，我们还尝试减少长期激素治疗，并保留睾丸部分。