Martindale B
St Charles Hospital, London.
Br J Psychiatry. 1987 Mar;150:319-23. doi: 10.1192/bjp.150.3.319.
The autosomal dominant mode of inheritance of Huntington's Chorea (HC) has been established for over 100 years. Strong psychological defences against the acceptance of this knowledge are commonly found both in professionals and in Huntington families and relatives who are at risk. One consequence of maintaining these defences is the continuing transmission of the gene, and therefore the disease, to succeeding generations. The defences of professional persons protect them from the difficult and unsettling task of providing genetic counselling to healthy relatives at risk. An increase in awareness of the psychodynamics involved may lead to constructive thinking about the current deficiencies in care and counselling services provided for these families.
亨廷顿舞蹈症（HC）的常染色体显性遗传模式已确立100多年。在专业人士以及有患病风险的亨廷顿家族和亲属中，普遍存在对接受这一事实的强烈心理防御。维持这些防御的一个后果是该基因，进而这种疾病，持续传递给后代。专业人士的防御使他们免于向有风险的健康亲属提供遗传咨询这一艰巨且令人不安的任务。对其中涉及的心理动力学认识的提高，可能会促使人们对目前为这些家庭提供的护理和咨询服务的不足进行建设性思考。
