Mubita Lynn, Seidman Michael, Rock Jack
Department of Neurosurgery, Henry Ford Hospital, Detroit, Michigan, USA.
Department of Otolaryngology, Henry Ford Hospital, Detroit, Michigan, USA.
Surg Neurol Int. 2018 Mar 19;9:64. doi: 10.4103/sni.sni_412_17. eCollection 2018.
Exostoses of the internal auditory canal is a rare finding that may present with disabling symptoms of dizziness, hearing loss, and vestibular dysfunction based on the extent of cranial nerve compression. The purpose of this case report is to discuss the presentation and outcomes in a patient who presented with this disorder.
A 19-year-old female presented to the neurotologist with left ear discomfort, pain with left lateral gaze, and dizziness. She underwent extensive evaluation including audiometric testing, videonystagmography, and neuroimaging, which confirmed left auditory and vestibular hypofunction and compression of the contents of the internal auditory canal from the exostosis. After extensive counseling, the patient elected to undergo a suboccipital craniectomy to remove the internal auditory canal exostosis. She experienced complete resolution of symptoms.
Exostoses of the internal auditory canal, although rare, can present with severe symptoms of dizziness, hearing loss, and vestibular hypofunction based on the extent of cranial nerve compression. Imaging, particularly with thin-cut computed tomography, is invaluable in making the correct diagnosis. Severe cases can be treated successfully with surgery with minimal or no complications and excellent outcome.
内耳道骨瘤是一种罕见的发现，根据颅神经受压程度，可能会出现头晕、听力丧失和前庭功能障碍等致残症状。本病例报告的目的是讨论一名患有这种疾病的患者的临床表现和治疗结果。
一名19岁女性因左耳不适、向左凝视时疼痛和头晕就诊于神经耳科医生。她接受了包括听力测试、视频眼震图和神经影像学在内的广泛评估，结果证实左耳听觉和前庭功能减退，内耳道骨瘤压迫内耳道内容物。经过充分的咨询后，患者选择接受枕下颅骨切除术以切除内耳道骨瘤。她的症状完全缓解。
内耳道骨瘤虽然罕见，但根据颅神经受压程度，可出现头晕、听力丧失和前庭功能减退等严重症状。影像学检查，尤其是薄层计算机断层扫描，对于做出正确诊断非常重要。严重病例可通过手术成功治疗，并发症极少或无并发症，且预后良好。
