母细胞性浆细胞样树突状细胞肿瘤
Blastic plasmacytoid dendritic cell neoplasm.
作者信息
Rai Manoj Ponadka, Bedi Prabhjot Singh, Kandola Samanjit Kaur, Kavuturu Shilpa, Singhal Rashi
机构信息
Michigan State University/Sparrow Hospital 788 Service Road, B301 Clinical Center East Lansing Michigan 48824.
UPMC East 2775 Mosside Blvd Monroeville Pennsylvania 15146.
出版信息
Clin Case Rep. 2018 Mar 4;6(4):770-772. doi: 10.1002/ccr3.1457. eCollection 2018 Apr.
Blastic plasmacytoid dendritic cell neoplasm is an aggressive neoplasm with a median survival of only a few months despite treatment. An exhaustive immunohistochemical workup is required to differentiate it from myeloid sarcoma and extranodal NK/T cell lymphoma. Treatment is with induction using a regimen utilized for leukemia. Allogeneic hematopoietic stem cell transplantation is recommended for those who achieve remission following induction.
母细胞性浆细胞样树突状细胞肿瘤是一种侵袭性肿瘤，尽管接受了治疗，其平均生存期仅为几个月。需要进行详尽的免疫组织化学检查以将其与髓系肉瘤和结外NK/T细胞淋巴瘤相鉴别。治疗采用用于白血病的诱导方案。对于诱导治疗后达到缓解的患者，建议进行异基因造血干细胞移植。
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