Aydin Sahin Derya, Vefa Yildirim Selman, Ozkan Murat
Department of Pediatric Cardiology, Mersin City Hospital, Mersin, Turkey.
Pediatric Cardiology Division, Pediatrics Department, Near East University, Nicosia, Cyprus.
Echocardiography. 2018 May;35(5):757-759. doi: 10.1111/echo.13883. Epub 2018 Apr 12.
Congenital left atrial appendage aneurysm (LAAA) is a very rare condition and occurs as a result of congenital dysplasia of musculi pectinate. These patients may be asymptomatic and/or may present with dyspnea, and thromboembolic events. The most common complications are life-threatening thromboembolic events and supraventricular tachyarrhythmias. Transthoracic echocardiography plays a very important role in the diagnosis of LAAA. Herein, we present a rare case of giant congenital LAAA.
先天性左心耳动脉瘤(LAAA)是一种非常罕见的疾病,由梳状肌先天性发育异常引起。这些患者可能无症状和/或可能出现呼吸困难以及血栓栓塞事件。最常见的并发症是危及生命的血栓栓塞事件和室上性快速心律失常。经胸超声心动图在LAAA的诊断中起着非常重要的作用。在此,我们报告一例罕见的巨大先天性LAAA病例。