van Ahlen H, Brühl P
Kinderurologie der Urologischen Klinik, Rheinischen Friedrich-Wilhelms-Universität Bonn.
Urologe A. 1988 Jul;27(4):207-13.
The recent literature is reviewed and the etiology, pathogenesis, diagnosis, therapy and prognosis of prune belly syndrome are presented and illustrated with reference to personal experience in typical cases. It seem possible that the syndrome is not an entity in its own right, since it also appears in incomplete forms. Prenatal sonography allows an early diagnosis, but to date intrauterine treatment is not indicated. Postnatal operative intervention in the form of major reconstructive surgery has to be viewed very critically. So far, no positive effects on long-term prognosis have been proven, so that, depending upon the severity of the syndrome, treatment should be as conservative as possible.
本文回顾了近期文献，并结合典型病例的个人经验，阐述了梅干腹综合征的病因、发病机制、诊断、治疗及预后，并举例说明。该综合征似乎并非独立存在的疾病实体，因为它也有不完全形式。产前超声检查可实现早期诊断，但迄今为止，不建议进行宫内治疗。对于以大型重建手术形式进行的产后手术干预，必须持非常谨慎的态度。到目前为止，尚未证实对长期预后有积极影响，因此，根据综合征的严重程度，治疗应尽可能保守。
