Fells P, Collin J R
Trans Ophthalmol Soc U K (1962). 1979 Apr;99(1):192-6.
This rare condition, an oculomotor palsy which is interrupted by spastic contractions of the levator muscle and the pupillary sphincter at fairly regular intervals, had been reported in 54 patients up to 1975. Two patients presented to the authors with apparently complete unilateral ptosis but abnormal pupillary reactions prompted closer examination. Once the diagnosis has been considered only 5 minutes of careful clinical examination are necessary to confirm or reject it. During the past 4 years the authors have found nine new cases of the condition and it is clear that the diagnosis must often be missed. Details of the patients are shown and discussed in the light of Loewenfeld and Thompson's theory of the pathology. The place of surgical treatment is considered.
这种罕见病症是一种动眼神经麻痹,提上睑肌和瞳孔括约肌会以相当规律的间隔出现痉挛性收缩,截至1975年已有54例相关病例报道。两位患者前来就诊时表现为明显的单侧上睑完全下垂,但异常的瞳孔反应促使进行了更仔细的检查。一旦考虑到这种诊断,仅需5分钟的仔细临床检查即可确诊或排除。在过去4年中,作者发现了9例该病症的新病例,显然这种诊断常常会被漏诊。现将患者的详细情况根据洛温费尔德和汤普森的病理学理论进行展示和讨论。同时也对手术治疗的作用进行了考量。