School of Cellular and Molecular Medicine, University of Bristol, UK.
Bristol Royal Hospital for Children, UK.
Haematologica. 2018 Sep;103(9):1493-1501. doi: 10.3324/haematol.2017.186700. Epub 2018 May 17.
Current therapies for childhood T-cell acute lymphoblastic leukemia have increased survival rates to above 85% in developed countries. Unfortunately, some patients fail to respond to therapy and many suffer from serious side effects, highlighting the need to investigate other agents to treat this disease. Parthenolide, a nuclear factor kappa (κ)B inhibitor and reactive oxygen species inducer, has been shown to have excellent anti-cancer activity in pediatric leukemia xenografts, with minimal effects on normal hemopoietic cells. However, some leukemia initiating cell populations remain resistant to parthenolide. This study examined mechanisms for this resistance, including protective effects conferred by bone marrow stromal components. T-cell acute leukemia cells co-cultured with mesenchymal stem cells demonstrated significantly enhanced survival against parthenolide (73±11%) compared to cells treated without mesenchymal stem cell support (11±9%). Direct cell contact between mesenchymal cells and leukemia cells was not required to afford protection from parthenolide. Mesenchymal stem cells released thiols and protected leukemia cells from reactive oxygen species stress, which is associated with parthenolide cytotoxicity. Blocking cystine uptake by mesenchymal stem cells, using a small molecule inhibitor, prevented thiol release and significantly reduced leukemia cell resistance to parthenolide. These data indicate it may be possible to achieve greater toxicity to childhood T-cell acute lymphoblastic leukemia by combining parthenolide with inhibitors of cystine uptake.
目前,儿童 T 细胞急性淋巴细胞白血病的治疗方法已使发达国家的存活率提高到 85%以上。不幸的是,一些患者对治疗没有反应,许多人还遭受严重的副作用,这突出表明需要研究其他药物来治疗这种疾病。小白菊内酯是一种核因子 kappa(κ)B 抑制剂和活性氧诱导剂,已被证明在儿科白血病异种移植物中具有出色的抗癌活性,对正常造血细胞的影响很小。然而,一些白血病起始细胞群仍然对小白菊内酯有抗性。本研究检查了这种抗性的机制,包括骨髓基质成分赋予的保护作用。与没有间充质干细胞支持的细胞相比,与间充质干细胞共培养的 T 细胞急性白血病细胞对小白菊内酯(73±11%)的存活明显增强(11±9%)。间充质细胞和白血病细胞之间不需要直接细胞接触即可提供对小白菊内酯的保护。间充质干细胞释放巯基并保护白血病细胞免受与小白菊内酯细胞毒性相关的活性氧应激。用小分子抑制剂阻断间充质干细胞摄取胱氨酸可防止巯基释放,并显著降低白血病细胞对小白菊内酯的耐药性。这些数据表明,通过将小白菊内酯与胱氨酸摄取抑制剂联合使用,可能实现对儿童 T 细胞急性淋巴细胞白血病更大的毒性。