Tas Betul, Çağlar Aysel, Altinay Serdar
Dr. Tas is with the Health Sciences University, Istanbul Bagcilar Research and Training Hospital, Department of Dermatology in Istanbul, Turkey.
Dr. Çağlar is with the Health Sciences University, Istanbul Bagcilar Research and Training Hospital, Department of Pathology in Istanbul, Turkey.
J Clin Aesthet Dermatol. 2018 May;11(5):43-47. Epub 2018 May 1.
We present the case of a 15-year-old girl who presented with an unusual grouping of lesions on her upper left leg. The lesions had been present since birth. The patient had five different types of lesions: 1) transparent grouped or scattered yellowish vesicles; 2) keratotic-surfaced, grouped dark-yellowish papules; 3) bright-red grouped papules; 4) keratotic-surfaced grouped dark-red papules; and 5) patchy, punctate, and erythematous red macules. All of the lesions were intertwined along the lines of Blaschko and were in the form of irregular serpiginous plaques. Histopathological examinations of the lesions showed three main histological features, and diagnoses of the lesions were made as lymphangioma circumscriptum, lymphangiokeratoma, and verrucous hemangioma. To the best of our knowledge, such intertwined lesions have never been reported in the literature. Hence, we suggest that the name of this unique combination of lesions be "congenital nevoid mixed hemato-lymphangio-keratoma serpiginosum."
我们报告一例15岁女孩，其左上腿出现了一组不同寻常的皮损。这些皮损自出生就存在。患者有五种不同类型的皮损：1）透明的、成簇或散在的淡黄色水疱；2）表面角化的、成簇的深黄色丘疹；3）鲜红色成簇丘疹；4）表面角化的、成簇的暗红色丘疹；5）斑片状、点状和红斑性红色斑疹。所有皮损均沿Blaschko线相互交织，呈不规则匐行性斑块状。皮损的组织病理学检查显示出三个主要组织学特征，病变诊断为局限性淋巴管瘤、淋巴管角化瘤和疣状血管瘤。据我们所知，这种相互交织的皮损在文献中从未有过报道。因此，我们建议将这种独特的皮损组合命名为“先天性痣样混合血液-淋巴管-角化瘤匐行疹”。
