Sellami Khadija, Mseddi Madiha, Snoussi Mouna, Gharbi Hela, Frikha Faten, Salah Rayda Ben, Jallouli Moez, Marzouk Sameh, Masmoudi Abderrahmen, Bahloul Zouhir, Turki Hamida
Dermatology Department, Hedi Chaker University Hospital, Sfax, Tunisia.
Internal Medicine Department, Hedi Chaker University Hospital, Sfax, Tunisia.
Rom J Intern Med. 2018 Dec 1;56(4):243-249. doi: 10.2478/rjim-2018-0015.
The prognosis of dermatomyositis (DM)/ polymyositis (PM) in adults is partly related to their association with neoplasia. The aim of our study was to report the epidemiologic, clinical, paraclinical, therapeutic and evolutionary aspects of DM associated with malignancy in patients from Sfax, south eastern of Tunisia.
A retrospective cohort study of patients with DM or PM admitted in Dermatology and Internal Medicine Departments of Hedi Chaker University Hospital of Sfax between 1996 and 2015. Cases of DM or PM associated with malignancy were retained.
Seventeen cases (13.5%) of DM or PM associated with malignancy were noted. Fourteen patients had DM and 3 patients had PM. The Sex ratio M / F was 0.3 and the mean age at diagnosis was 56.5 years. In DM patients, malignancy preceded the myositis in 64.2% of cases. In PM patients, only one patient was known to have breast cancer and the myositis revealed the cancer for 2 others. Treatment consisted of corticosteroids associated with methotrexate in 4 cases. Outcome was fatal in 5 cases (29.4%), due to the underlying cancer in 3 cases. Swallowing disorders related to DM/PM were responsible for death in 2 cases.
There are no specific clinical or biological features in paraneoplastic DM. In our series, breast neoplasm represented the first cancer associated with DM. Cancers of nasopharynx, colon and urinary tract had the second position.
成人皮肌炎(DM)/多发性肌炎(PM)的预后部分与其合并肿瘤有关。我们研究的目的是报告突尼斯东南部斯法克斯地区DM合并恶性肿瘤患者的流行病学、临床、副临床、治疗及病情演变方面的情况。
对1996年至2015年间在斯法克斯市赫迪·查克大学医院皮肤科和内科住院的DM或PM患者进行回顾性队列研究。纳入DM或PM合并恶性肿瘤的病例。
共记录到17例(13.5%)DM或PM合并恶性肿瘤的病例。其中14例为DM患者,3例为PM患者。男女比例为0.3,诊断时的平均年龄为56.5岁。在DM患者中,64.2%的病例恶性肿瘤先于肌炎出现。在PM患者中,仅1例已知患有乳腺癌,另外2例的肌炎发现了癌症。4例患者的治疗包括皮质类固醇联合甲氨蝶呤。5例(29.4%)患者预后不良,3例死于潜在癌症,2例死于与DM/PM相关的吞咽障碍。
副肿瘤性DM没有特定的临床或生物学特征。在我们的系列研究中,乳腺肿瘤是与DM相关的首要癌症。鼻咽癌、结肠癌和泌尿系统癌症位居第二。