[Diagnosis and surgical reconstruction results for 14 cases of patients with congenital ossicular chain malformation].

To investigate the diagnosis of common congenital ossicular chain malformation and the efficacy of ossicular chain reconstruction. Fourteen cases with 15 ears of congenital ossicular chain malformation were included, consisting of 10 cases unilateral conductive hearing loss(10 ears), 1 case bilateral conductive hearing loss (2 ears) and 3 cases unilateral mixed hearing loss with significant conductive hearing loss(3 ears). Tympanoplasty was proceed on all 15 ears, 1 ear was proceed by loosen the cartilage fixation of ossicular chain and tympanic cavity wall. Fourteen ears were proceed with ossicular chain reconstruction, including 3 ears with TORP,10 ears with PORP and 1 ear with artificial stapes operation. The efficacy was measured by comparing the values of air bone gap(ABG) before and after the operation. The average ABG of pre-operation was 39.9 dB, the ABG for 3 week and 6 to 8 months after operation were 22.3 dB and 19.6 dB, which were 17.6 dB and 20.3 dB improve respectively(=22.10, <0.01 and =12.813，<0.01). Operation is the first choice for those conductive hearing loss causing by simple congenital ossicular chain malformation, relevant ossicular chain reconstruction due to particular situation of the surgery can significantly improve hearing.