继发性淀粉样变性与囊性纤维化。五例病例的形态学和组织化学研究。
Secondary amyloidosis and cystic fibrosis. A morphological and histochemical study of five cases.
作者信息
Bontempini L, Ghimenton C, Colombari R, Malena M, Iuzzolino P, Canciani M, Doglioni C, Sbabo L
机构信息
Serv. di Anatomia e Istologia Patologica, Ospedale Borgo Trento, Verona, Italy.
出版信息
Histol Histopathol. 1987 Oct;2(4):413-6.
The pathological findings of five cases of amyloidosis associated with Cystic Fibrosis are reported. Rectal biopsy led to the diagnosis of amyloidosis in four patients. In three cases the diagnosis was confirmed at autopsy, with involvement of spleen, liver, kidneys, adrenal glands, thyroid and other organs. It seems that Secondary Amyloidosis provokes a significant, although rare, complication of Cystic Fibrosis as greater numbers of these patients survive into adulthood.
报告了5例与囊性纤维化相关的淀粉样变性病例的病理结果。直肠活检使4例患者诊断为淀粉样变性。3例在尸检时确诊，累及脾脏、肝脏、肾脏、肾上腺、甲状腺和其他器官。随着越来越多的囊性纤维化患者存活至成年，继发性淀粉样变性似乎引发了一种虽罕见但严重的并发症。
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