眼眶区域未分化多形性肉瘤：一例报告
Undifferentiated pleomorphic sarcoma of the orbital region: a case report.
作者信息
Cruz Natasha Ferreira Santos da, Matsuno Carolina Ando, Cruz Sérgio Ferreira Santos da, Miranda Aline Pimentel de, Vital Filho José
机构信息
Ophthalomology Department, Irmandade da Santa Casa de Misericórdia de São Paulo, São Paulo, SP, Brazil.
Universidade do Estado do Pará, Belém, PA, Brazil.
出版信息
Arq Bras Oftalmol. 2018 Apr;81(2):153-156. doi: 10.5935/0004-2749.20180033.
Undifferentiated pleomorphic sarcoma (UPS) is an extremely rare tumor that occurs in the head and neck region. Here, we report a unique case of a primary undifferentiated pleomorphic sarcoma in the orbital region. A 35-year-old woman presented with a progressive proptosis and periocular edema for 1 year. She had no previous history of surgery, skin malignancy, or radiation. Imaging tests showed an extraconal mass, not involving the muscles. The tumor was surgically removed and adjuvant radiotherapy was required after histological examination, which showed an undifferentiated pleomorphic sarcoma of the orbit. There was no recurrence after 1 year of follow-up. Though rare, undifferentiated pleomorphic sarcoma should be included in the differential diagnoses of orbital tumors.
未分化多形性肉瘤（UPS）是一种极其罕见的肿瘤，发生于头颈部区域。在此，我们报告一例发生于眼眶区域的原发性未分化多形性肉瘤的独特病例。一名35岁女性因渐进性眼球突出和眼周水肿1年就诊。她既往无手术史、皮肤恶性肿瘤病史或放疗史。影像学检查显示眶锥外肿块，未累及肌肉。肿瘤经手术切除，组织学检查显示为眼眶未分化多形性肉瘤，术后需辅助放疗。随访1年无复发。尽管罕见，但未分化多形性肉瘤应纳入眼眶肿瘤的鉴别诊断。
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