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嗜铬细胞瘤,“伟大的伪装者”,在一名年轻患者中表现为严重急性失代偿性心力衰竭。

Pheochromocytoma, "the Great Masquerader," Presenting as Severe Acute Decompensated Heart Failure in a Young Patient.

作者信息

Reyes Hans A, Paquin Jason J, Harris David M

机构信息

Division of Cardiovascular Health and Disease, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Division of Cardiology, Mercy Heart Institute, Cincinnati, OH, USA.

出版信息

Case Rep Cardiol. 2018 Apr 29;2018:8767801. doi: 10.1155/2018/8767801. eCollection 2018.

DOI:10.1155/2018/8767801
PMID:29854474
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5949188/
Abstract

A 22-year-old man presented to the hospital with progressive shortness of breath, chest discomfort, sinus tachycardia, and emesis. The echocardiogram demonstrated global hypokinesis with a left ventricle ejection fraction of 15-20%. The patient was treated for acute systolic heart failure decompensation with diuresis and afterload reduction. Unexpectedly, an abdominal computed tomography showed a left adrenal mass and subsequent serum/urine metanephrine tests suggested pheochromocytoma. Once the patient had stabilized, he underwent an uneventful adrenalectomy with histology results confirming the diagnosis of pheochromocytoma. After six months follow-up, he is currently doing well with close outpatient follow-up by cardiology.

摘要

一名22岁男性因进行性气短、胸部不适、窦性心动过速和呕吐入院。超声心动图显示全心运动减弱,左心室射血分数为15%-20%。患者接受了利尿和减轻后负荷治疗急性收缩性心力衰竭失代偿。意外的是,腹部计算机断层扫描显示左肾上腺肿块,随后的血清/尿间甲肾上腺素检测提示嗜铬细胞瘤。患者病情稳定后,顺利接受了肾上腺切除术,组织学结果证实为嗜铬细胞瘤。经过六个月的随访,他目前情况良好,由心脏病学门诊密切随访。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/ecfbc10b8c0c/CRIC2018-8767801.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/89dcfbf440fb/CRIC2018-8767801.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/7590be5b3950/CRIC2018-8767801.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/ecfbc10b8c0c/CRIC2018-8767801.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/89dcfbf440fb/CRIC2018-8767801.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/7590be5b3950/CRIC2018-8767801.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a254/5949188/ecfbc10b8c0c/CRIC2018-8767801.003.jpg

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