Mital P D, Abhijit K, Shishir G
Department of Nephrology, Muljibhai Patel Urological Hospital, Nadiad, Gujarat, India.
Indian J Nephrol. 2018 Mar-Apr;28(2):167-169. doi: 10.4103/ijn.IJN_330_16.
Hypertension is a frequent early manifestation of autosomal dominant polycystic kidney disease (ADPKD). Many mechanisms cause hypertension in ADPKD; however, primary aldosteronism (PA) as a possible manifestation of hypertension in ADPKD is extremely rare. The diagnosis of PA in ADPKD is extremely challenging because multiple renal cysts can mask the identification of adrenal adenomas, and ADPKD is associated with hypertension in majority of cases. Here, we report a unique case of a young lady with ADPKD with hypertension masquerading PA.
高血压是常染色体显性多囊肾病（ADPKD）常见的早期表现。ADPKD中导致高血压的机制有多种；然而，作为ADPKD高血压可能表现形式的原发性醛固酮增多症（PA）极为罕见。ADPKD中PA的诊断极具挑战性，因为多个肾囊肿会掩盖肾上腺腺瘤的识别，而且大多数情况下ADPKD都与高血压相关。在此，我们报告一例独特病例，一名患有ADPKD且高血压伪装成PA的年轻女性。
