Belczak Sergio Quilici, Klajner Rafael Kogan, Ogawa Lara Cote, Lucato Laís Leite, Zeque Bruna Stecca, de Macedo Felipe Basso, da Silva Ingredy Tavares, Atihe Luís Felipe
Instituto Belczak de Cirurgia Vascular e Endovascular, São Paulo, SP, Brasil.
Centro Universitário São Camilo - CUSC, São Paulo, SP, Brasil.
J Vasc Bras. 2016 Jul-Sep;15(3):239-244. doi: 10.1590/1677-5449.001016.
Ehlers-Danlos syndrome is a genetic disease that results in abnormalities of collagen synthesis, causing extremely fragile connective tissue. This fragility predisposes patients to a series of vascular disorders, such as dissections, aneurysms and pseudoaneurysms. The authors describe the case of a 19-year-old patient with an aneurysm of the brachiocephalic trunk who was treated endovascularly by placement of covered stents. The case progressed with complications at the puncture site, which was also treated on an emergency basis, using endovascular techniques with a covered stent.
埃勒斯-当洛综合征是一种导致胶原蛋白合成异常的遗传性疾病,会造成结缔组织极度脆弱。这种脆弱性使患者易患一系列血管疾病,如夹层动脉瘤、真性动脉瘤和假性动脉瘤。作者描述了一名19岁头臂干动脉瘤患者的病例,该患者通过植入覆膜支架进行血管内治疗。该病例在穿刺部位出现并发症,也采用血管内技术植入覆膜支架进行了紧急治疗。