Terro Wahid, Hamadeh Nizar, Terro Miray
Oral & Maxillofacial Surgery Division, Dental School, Tutor Beirut Arab University (BAU), Beirut, Lebanon.
Dept. Oral & Maxillofacial Surgery, Dental School, Chief of Clinic Lebanese University (LU), Beirut, Lebanon.
J Surg Case Rep. 2018 Jun 15;2018(6):rjy089. doi: 10.1093/jscr/rjy089. eCollection 2018 Jun.
Dermatofibrosarcoma protuberans (DFSP) is a rare neoplasm which represents <0.1% of all tumors but it is considered the most common skin sarcoma. It is a slow-growing tumor that arises from the dermis and invades deeper tissues. The precise origin of DFSP is not well known. It is most frequently seen on the trunk, extremities, and head and neck. The standard treatment of the localized huge DFSP consists of a wide local surgical resection with recommended surgical margins of 2-3 cm. Local recurrence after incomplete excision is common. We present a case of 35-year-old man with enormous bulky mass on the face. Upon histological examination, the diagnosis of DFSP was made, and the patient underwent en bloc wide local excision of the mass followed by the use of Trapezius musculocutaneous pedicle flap reconstruction. On 32 months follow-up, no recurrence has been reported.
隆突性皮肤纤维肉瘤（DFSP）是一种罕见的肿瘤，占所有肿瘤的比例不到0.1%，但它被认为是最常见的皮肤肉瘤。它是一种生长缓慢的肿瘤，起源于真皮并侵犯更深层组织。DFSP的确切起源尚不清楚。它最常见于躯干、四肢以及头颈部。局限性巨大DFSP的标准治疗方法是广泛的局部手术切除，推荐的手术切缘为2 - 3厘米。不完全切除后局部复发很常见。我们报告一例35岁男性患者，面部有巨大肿块。经组织学检查，诊断为DFSP，患者接受了肿块的整块广泛局部切除，随后采用带蒂斜方肌肌皮瓣重建。在32个月的随访中，未报告复发情况。
