Zablah Jenny E, Ross Michael, Wilson Neil, Fonseca Brian, Mitchell Max B
1 Interventional Cardiology, Children's Hospital of Colorado, Heart Institute, Aurora, CO, USA.
2 Children's Hospital of Colorado, Heart Institute, Aurora, CO, USA.
World J Pediatr Congenit Heart Surg. 2018 Jul;9(4):451-453. doi: 10.1177/2150135118769326.
Single ventricle patients with interrupted inferior vena cava (IVC) and azygos continuation to the superior vena cava (SVC) are typically palliated with a bidirectional cavopulmonary shunt (BCPS), known as the Kawashima operation in this setting. Because the volume of venous blood directed to the pulmonary arteries is substantially greater in the presence of interrupted IVC, Kawashima procedures are commonly delayed to older age compared to other single ventricle patients undergoing BCPS. We report two young infant single ventricle patients with interrupted IVC and azygos continuation to the SVC who underwent stage I Norwood procedures for initial palliation. In both cases, a fenestrated hemi-Fontan procedure achieved successful Kawashima circulations.
下腔静脉中断（IVC）且奇静脉延续至上腔静脉（SVC）的单心室患者通常采用双向腔肺分流术（BCPS）进行姑息治疗，在这种情况下该手术被称为川岛手术。由于存在下腔静脉中断时流向肺动脉的静脉血量显著增加，与接受BCPS的其他单心室患者相比，川岛手术通常会推迟到患者年龄较大时进行。我们报告了两名患有下腔静脉中断且奇静脉延续至上腔静脉的单心室幼儿患者，他们接受了一期诺伍德手术进行初始姑息治疗。在这两个病例中，开窗半Fontan手术均成功实现了川岛循环。
