Reddy S, Swamy R, Irugu D V Kumar, Ramji K V V
Department of Otorhinolaryngology & Head and Neck Surgery, Govt ENT Hospital, Osmania Medical College, Hyderabad, India.
Department of Otorhinolaryngology & Head and Neck Surgery, All India Institute of Medical Sciences, New Delhi, India.
Acta Otorhinolaryngol Ital. 2018 Apr;38(2):170-173. doi: 10.14639/0392-100X-1278.
Inflammatory myofibroblastic tumours (IMTs) are rare and clinically benign in childhood, and malignant in adults. The aetiology of IMTs is not clear, and recent studies report it as true neoplasm rather than a reactive or inflammatory lesion. IMTs can involve any part of the body, but are usually common in lungs. These are rarely seen in adults and tracheal involvement is also rare in both adults and children. We describe an 18-year-old woman who presented with respiratory difficulty to the emergency department. On clinical examination, the patient had complete absence of breath sounds on the right side of the chest. CT of the chest and virtual bronchoscopy revealed a polypoidal soft tissue mass lesion involving the carina with occlusion of right main bronchus. Endoscopic-assisted resection was performed under general anaesthesia and the final pathological diagnosis was tracheal IMT.
炎性肌纤维母细胞瘤(IMTs)在儿童期罕见且临床呈良性,在成人中则为恶性。IMTs的病因尚不清楚,最近的研究将其报告为真正的肿瘤而非反应性或炎性病变。IMTs可累及身体的任何部位,但通常常见于肺部。在成人中很少见,气管受累在成人和儿童中也很罕见。我们描述了一名18岁女性,她因呼吸困难到急诊科就诊。临床检查时,患者右侧胸部完全没有呼吸音。胸部CT和虚拟支气管镜检查显示一个息肉样软组织肿块病变累及隆突,右主支气管闭塞。在全身麻醉下进行了内镜辅助切除术,最终病理诊断为气管IMT。