Slim D, Gunawardena H, Calvert J M, Daly R S, Plummeridge M J, Medford A R
North Bristol Lung Centre, Southmead Hospital, Bristol, UK.
North Bristol Lung Centre & University of Bristol, Brunel Building, Southmead Hospital, Westbury-on-Trym, Bristol BS10 5NB, UK,
J R Coll Physicians Edinb. 2018 Jun;48(2):130-133. doi: 10.4997/JRCPE.2018.207.
IgG4-related disease is an immune-mediated fibro-inflammatory disease, characterised by distinct pathological features. An increasing number of clinical phenotypes are described, from single-organ disease to a multisystem disorder, which can present to a variety of different specialities. Recognition is key; its protean manifestations can mimic other inflammatory diseases, infection and malignancy. Here, we present three cases to highlight the importance of being familiar with this condition in its various forms.
IgG4相关性疾病是一种免疫介导的纤维炎症性疾病,具有独特的病理特征。越来越多的临床表型被描述出来,从单器官疾病到多系统疾病,可累及各种不同的专科。认识是关键;其多样的表现可模仿其他炎症性疾病、感染和恶性肿瘤。在此,我们呈现三例病例以强调熟悉这种疾病各种形式的重要性。