黄斑下硬化性毛细血管瘤
Submacular sclerosing capillary hemangioblastoma.
作者信息
Hamza Hany S, Elhusseiny Abdelrahman M
机构信息
Ophthalmology Department, Kasr Al Ainy School of Medicine, Cairo University, Egypt.
出版信息
Am J Ophthalmol Case Rep. 2018 Jun 2;11:61-63. doi: 10.1016/j.ajoc.2018.05.010. eCollection 2018 Sep.
PURPOSE
To report a case of submacular cystic lesion that turned out to be a sclerosing capillary hemangioblastoma. The retinal capillary hemangioblastoma may arise as a part of von Hippel-Lindau syndrome however, they may occur as an isolated entity , but submacular capillary hemangioblastoma has never been reported.
OBSERVATIONS
A case of a 56-year-old female who presented with a right yellow submacular lesion. The mass was excised via pars-plana vitrectomy and histopathological assessment revealed a submacular sclerosing capillary hemangioblastoma.
CONCLUSION
and importance: The capillary hemangioblastoma is a benign vascular tumor that may arise submacularly and is not necessarily associated with von Hippel-Lindau disease. It is difficult to be differentiated clinically from other submacular lesions but the possibility should be considered.
目的
报告一例黄斑下囊性病变，结果为硬化性毛细血管性血管母细胞瘤。视网膜毛细血管性血管母细胞瘤可能作为冯·希佩尔-林道综合征的一部分出现，然而，它们也可能作为孤立的实体发生，但黄斑下毛细血管性血管母细胞瘤从未有过报道。
观察结果
一名56岁女性患者，出现右黄斑下黄色病变。通过玻璃体切除术切除肿块，组织病理学评估显示为黄斑下硬化性毛细血管性血管母细胞瘤。
结论及重要性
毛细血管性血管母细胞瘤是一种良性血管肿瘤，可发生于黄斑下，不一定与冯·希佩尔-林道病相关。临床上很难将其与其他黄斑下病变区分开来，但应考虑到这种可能性。
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