Pagès M, Pagès A M
Ann Pathol. 1985;5(3):205-7.
A sural nerve biopsy was performed in a case of adrenomyeloneuropathy which was confirmed by biochemical investigations. Morphometric study of the nerve revealed a loss of large myelinated fibers with signs of demyelination, and normal unmyelinated fibers. Electron microscopic study showed typical lipid inclusions in some histiocytes and Schwann cells. The interest of nerve biopsy in histopathological diagnosis of adrenomyeloneuropathy is emphasized.
对一例经生化检查确诊的肾上腺脑白质营养不良症患者进行了腓肠神经活检。神经的形态计量学研究显示，有髓大纤维减少并伴有脱髓鞘迹象，而无髓纤维正常。电子显微镜研究显示，一些组织细胞和施万细胞中有典型的脂质包涵体。强调了神经活检在肾上腺脑白质营养不良症组织病理学诊断中的意义。
